Adenocarcinoma mucinoso de quiste gigante de uraco asociado a pseudomixoma peritoneal
- Carvajal Balaguera, J. 1
- Martín García-Almenta, M. 1
- Martín García-Almenta, E. 2
- Albeniz Aquiriano, L. 3
- Simón Cirujano, F. 4
- Cerquella Hernández, C.M. 1
- 1 Hospital Central Cruz Roja. Servicio de Cirugía General y Digestiva
- 2 Hospital Clínico San Carlos. Servicio de Cirugía General y Digestiva
- 3 Hospital Central Cruz Roja. Servicio Radiodiagnóstico
- 4 Hospital Central Cruz Roja. Servicio de Anestesia
ISSN: 1139-8264
Any de publicació: 2015
Volum: 18
Número: 4
Pàgines: 173-181
Tipus: Article
Altres publicacions en: Revista española de investigaciones quirúrgicas
Resum
Pseudomyxoma peritonei arising from mucinous adenocarcinoma of the urachus is an extremely rare condition. We identified 36 previous cases published to date.We report the case in a 51-year-old man, asymptomatic, presented as a finding on CT abdomen review after lithotripsy, a mass in the anterior wall urachal dependent. At laparotomy, the cystic mass, 10x8 cm, was could be completely separated from the bladder and was excised. It was smooth-walled and filled with thick mucinous fluid. A large volume of pseudomyxoma peritonei was present. Histology revealed an adenocarcinoma mucinous of the ura- chus associated with pseudomyxoma peritonei. After the first intervention was decided to reoperate the patient. Cytoreductive surgery and hyperthermic intraperitoneal chemotherapy was performed. The patient was well, with no tumour recurrence, at 6 months follow-up. We discuss aspects of embryology, epidemiology, clinical manifestations, diagnosis and treatment of this complex pat